Paolo Bernardi#

1. Bernardi, P. (1992) Modulation of the Mitochondrial Cyclosporin A-Sensitive Permeability Transition Pore by the Proton Electrochemical Gradient. Evidence that the Pore can be Opened by Membrane Depolarization. J Biol Chem 267, 8834-8839 - 261 citations (ISI)

2. Petronilli, V., Costantini, P., Scorrano, L., Colonna, R., Passamonti, S. and Bernardi, P. (1994) The Voltage Sensor ofthe Mitochondrial Permeability Transition Pore is Tuned by the Oxidation-Reduction State of Vicinal Thiols. Increase ofthe Gating Potential by Oxidants and its Reversal by Reducing Agents. J Biol Chem 269, 1663 8-16642 - 338 citations (ISI)

3. Nicolli, A., Basso, E., Petronilli, V., Wenger, R.M. and Bernardi, P. (1996) Interactions of Cyclophilin with the Mitochondrial Inner Membrane and Regulation of the Permeability Transition Pore, a Cyclosporin A-sensitive Channel. J Biol Chem 271, 2185-2192 – 268 citations (ISI)

4. Costantini, P., Chernyak, B.V., Petronilli, V. and Bernardi, P. (1996) Modulation of the Mitochondrial Permeability Transition Pore by Pyridine Nucleotides and Dithiol Oxidation at Two Separate Sites. J Biol Chem 271, 6746-675l - 263 citations (ISI)

5. Bernardi, P. (1999) Mitochondrial Transport of Cations: Channels, Exchangers and Permeability Transition. Physiol Rev 79, 1127-1155 - 659 citations (ISI)

6. Irwin, W., Bergamin, N., Sabatelli, P., Reggiani, C., Megighian, A., Merlini, L., Braghetta, P., Volpin, D., Bressan, G.M., Bernardi, P.*, and Bonaldo, P.* (2003) Mitochondrial dysfunction and apoptosis in rnyopathic mice with collagen VI deficiency, Nat Genet 35, 367-371 *Corresponding Authors [Covered in News and Views by Rizzuto (2003) Nat. Genet. 35, 300 and in an Editorial by Olsen Matrix Biology (2003) 22, 519] - 98 citations (ISI)

7. Basso, E., Fante, L., Fowlkes, J., Petronilli, V. Forte, M.A. and Bernardi, P. (2005) Properties of the Permeability Transition Pore in Mitochondria Devoid of Cyclophilin D, J Biol Chem 280, l8558-18561 [19th most read article in the Journal of Biological Chemistry in May, 2005; reviewed with top score (6, must read) in Faculg of 1000 Biology; commented upon by A. Gawrylewski, The Scientist (2007) 21, 73] - 182 citations (ISI)

8. Angelin, A., Tiepolo, T., Sabatelli, P., Grumati, P., Bergamin, N., Goliieri, C., Mattioli, E., Gualandi, F., Ferlini, A., Merlini, L., Maraldi, N.M., Bonaldo, P. and Bernardi, P. (2007) Mitochondrial dysfunction in the pathogenesis of Ullrich congenital muscular dystrophy and prospective therapy with cyclosporins, Proc Natl Acad Sci USA 104, 99l-996 [covered in an Editorial by Olsen, Matrix Biology (2007) 26, 145; reviewed (score 3, recommended) in Faculty of 1000 Medicine] - 41 citations (ISI)

9. Merlini, L., Angelin, A., Tiepolo, T., Braghetta, P., Sabatelli, P., Zarnparelli, A., Ferlini, A., Maraldi, N.M., Bonaldo, P. and Bernardi, P. (2008) Cyclosporin A corrects mitochondrial dysfunction and muscle apoptosis in patients with collagen VI myopathies, Proc Natl Acad Sci USA 105, 5225-5229 [covered in an Editorial by Olsen, Matrix Biology (2008) 27 273; reviewed by Robinson, Neurology Today, Nov 20, 2008, 22-23 and Kaplan (2008) Med. Sci. (Paris) 24, 470] - 37 citations (ISI)

l0. Giorgio, V., Bisetto, E., Soriano, M.E., Dabbeni-Sala, F., Basso, E., Petronilli, V., Forte, M.A., Bernardi, P.* and Lippe, G.* (2009) Cyclophilin D modulates mitochondrial FGF) ATP synthase by interacting with the lateral stalk of the complex, *Corresponding authors, J Biol Chem 284, 33982-33988 [reviewed with top score (6, must read) in Faculty of 1000 Biology]